Extraosseous Ewing Sarcoma (EES) is a rare subtype of Ewing Sarcoma which originates usually in soft tissues when compared to bones. We present the case of a 14-year-old boy presenting with an atypical painless swelling on the left side of the chest and pleural effusion. On evaluation that included clinical, histopathological and radiological led to a diagnosis of EES. We make a case to emphasize the importance of considering EES in differential diagnosis of thoracic masses particularly among paediatric patients and highlights the diagnostic challenges encountered with such rare presentations.
Keywords: Extraosseous ewing sarcoma, Chest, Tumours, Sarcoma