A rare presentation of extraosseous ewing sarcoma in a 14-year-old boy with pleural involvement

Raju, Rajesh; M. Arya, Sulbha; Raju, Ipshita; Prasad, Banuru; Saini, Sanjeev; Burugina Nagaraja, Sharath

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DOI 10.18231/j.ijpo.2025.042
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A rare presentation of extraosseous ewing sarcoma in a 14-year-old boy with pleural involvement

Author Details:

Rajesh Raju

Sulbha M. Arya

Ipshita Raju

Banuru Prasad ^*

Sanjeev Saini

Sharath Burugina Nagaraja

Indian Journal of Pathology and Oncology. 12(2):208-211, 2025. | 10.18231/j.ijpo.2025.042

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Extraosseous Ewing Sarcoma (EES) is a rare subtype of Ewing Sarcoma which originates usually in soft tissues when compared to bones. We present the case of a 14-year-old boy presenting with an atypical painless swelling on the left side of the chest and pleural effusion. On evaluation that included clinical, histopathological and radiological led to a diagnosis of EES. We make a case to emphasize the importance of considering EES in differential diagnosis of thoracic masses particularly among paediatric patients and highlights the diagnostic challenges encountered with such rare presentations.

Keywords: Extraosseous ewing sarcoma, Chest, Tumours, Sarcoma

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Indian Journal of Pathology and Oncology

A rare presentation of extraosseous ewing sarcoma in a 14-year-old boy with pleural involvement

Author Details: Rajesh Raju Sulbha M. Arya Ipshita Raju Banuru Prasad * Sanjeev Saini Sharath Burugina Nagaraja

References

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Author Details:

Rajesh Raju

Sulbha M. Arya

Ipshita Raju

Banuru Prasad ^*

Sanjeev Saini

Sharath Burugina Nagaraja