Primary mesenteric fibromatosis: Report of a sporadic case

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Case Report

Author Details : Soumya BM, Chandrasekhar HR, Sunil S. Byadgi, Vikram Y, Vardendra Kulkarni

Volume : 4, Issue : 1, Year : 2017

Article Page : 147-149

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Abstract

Mesenteric fibromatosis or intra-abdominal desmoid tumour is a rare neoplastic, monoclonal myofibroblastic proliferative disease affecting the mesentry which is prone to aggressive local recurrences, but lacks metastatic potential. Primary or spontaneous mesenteric fibromatosis is rare which occurs in absence of any predisposing conditions. Here, we report a case of a 66 year old male who presented with an abdominal mass. Abdominal examination revealed a firm mobile non-tender mass palpable in the lower portion of epigastrium. Ultrasonography showed a solid lesion of mesenteric origin. He underwent surgical excision of the mass with resection of involved small bowel and end to end anastomosis. Histopathology showed fascicles of bland spindle shaped cells with dilated blood vessels and keloidal collagen fibres. Immunohistochemistry showed β-catenin +ve, CD 117-ve and CD 34 –ve, which is confirmative of fibromatosis. Postoperative period was uneventful. Complementary therapies were not suggested in our patient as the tumour was a primary desmoid-type fibromatosis with complete resection and tumour free resection margins.

Keywords: Mesentery; Myofibroblasts; Fibromatosis, Abdominal; Immunohistochemistry; Beta catenin

How to cite : Soumya Bm, Chandrasekhar Hr, Byadgi S S, Vikram Y, Kulkarni V, Primary mesenteric fibromatosis: Report of a sporadic case. Indian J Pathol Oncol 2017;4(1):147-149

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